Proximal weakening?

[Guest guest]

Hi everyone...

I'm wondering out there if anyone has had problem's as a child with more

proximal weakening? Gavin now has marked weakening of his thigh and hip

adductor muscles on one side...He has just come through a big growth

spurt and has major fatigue...we are now getting him a power wheelchair

for evening riding around when going longer distances outside...he needs

to be independent and we can't keep pushing him in a stroller. It seems

to me that he is weakening faster than most...his back is weak too and

he tires holding himself upright. Oddly he doesn't have a ton of

footdrop nor has he major foot deformity...the neurologist said he is

weaker overall than typical 1A. Apparently it is possible that he has

more than just a triplicate copy of PMP22 (hence 1A)...but another more

type 2 gene activated also, although this hasn't been tested.

Any thoughts? Has anyone experience with power chairs?

Thanks

Sally