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American College of Rheumatology 1999 Annual

Scientific Meeting

[Medscape, 1999. © 1999 Medscape, Inc.]

Epidemiology, Diagnostics, and Management

Borenstein, MD

Sjogren syndrome was addressed in a State of the Art

Lecture by Roland

Jonsson, DMD,PhD, professor of immunology at the

University of Bergen

in

Norway. He reviewed the clinical manifestations and

research advances

associated with Sjogren syndrome and the presentation

of more than 40

abstracts.

Sjogren syndrome was named for the Swedish

ophthalmologist Henrik

Sjogren,

who first described the clinical and pathological

findings of

xerostomia

(dry mouth) and keratoconjunctivitis sicca (dry

eye).[1] Primary

Sjogren

syndrome is the disorder that occurs independent of

any additional

connective tissue disease, whereas secondary

Sjogren syndrome occurs in the setting of other

connective tissue

diseases,

such as rheumatoid arthritis, systemic lupus

erythematosus, or

polymyositis.

Epidemiology

Sjogren syndrome is a disease that affects all

populations throughout

the

world and occurs in all age groups. The peak incidence

is in the fourth

and

fifth decades of life, with a female-male ratio of

9:1. The prevalence

of

primary Sjogren syndrome varies from 0.08% in a

population study in

California to 2.7% in Sweden,[2,3] with an average

prevalence of 0.2%.

The

variation in frequency of the illness in these

population studies may

be

explained in part by different classification

criteria. The variation

in

other associated illnesses, such as lymphoma,

demyelinating disorders,

or

vasculitis, may also result from a lack of agreement

on diagnostic

criteria.

Classification Criteria

The most recent European criteria from 1993[4] include

an emphasis on

patients' subjective complaints. The criteria include

the presence of

four

of six symptoms, including (1) ocular symptoms, (2)

oral symptoms, (3)

evidence of keratoconjunctivitis sicca, (4) focal

sialadenitis by minor

salivary gland involvement, (5) instrumental evidence

of salivary gland

involvement, and (6) presence of autoantibodies.

Ocular symptoms include dry eyes for more than 3

months, recurrent

sensation

of sand or gravel in the eyes, or use of tear

substitutes more than

three

times a day. Oral symptoms include the daily feeling

of dry mouth for

more

than 3 months, recurrent or persistent swollen

salivary glands, or use

of

liquid to aid in swallowing dry food. Ocular signs are

characterized by

a

positive result on the Shirmer test (<5 mm in 5

minutes) or a Rose

Bengal

staining score of more than 4 according to the van

Bijsterveld scoring

system. Focal sialadenitis is distinguished by

lymphoid infiltration

in

exocrine glands.

The grading system of 1 to 4 corresponds to increasing

lymphocytic

infiltration with increasing destruction of salivary

gland structures.

Objective salivary gland testing includes salivary

scintigraphy,

parotid

sialography, or unstimulated salivary flow (<1.5 mL in

15 minutes).

Antibodies to Ro(SS-A) or La(SS-B), antinuclear

antibodies, and

rheumatoid

factors are associated with Sjogren syndrome. For

primary Sjogren

syndrome,

the presence of four of six criteria has a sensitivity

of 93.5% and

specificity of 94.0%.

The San Diego criteria for Sjogren syndrome include

manifestations of

both

primary and secondary Sjogren syndrome. Primary

Sjogren syndrome is

characterized by the following:

1. Symptoms and objective signs of ocular

dryness (Schirmer test

result of <8-mm wetting per 5 minutes and positive

Rose Bengal staining

of

cornea or conjunctiva to demonstrate

keratoconjunctivitis sicca).

2. Symptoms and objective signs of dry mouth

(decreased parotid

flow

rate using Lashley cups and abnormal findings on

biopsy specimen of

minor

salivary gland, with a focus score of >2 based on an

average of four

evaluable lobules).

3. Serologic evidence of systemic autoimmunity

(elevated

rheumatoid

factor >1:320 or elevated antinuclear antibody >1:320

or presence of

anti-SS-A[Ro] or anti-SS-B[La]antibodies).

Secondary Sjogren syndrome is defined by

characteristic signs and

symptoms

of Sjogren syndrome plus clinical features of

rheumatoid arthritis,

systemic

lupus erythematosus, polymyositis, scleroderma, or

biliary cirrhosis.

The

European and San Diego classification systems are the

two most

currently

referenced criteria.

Clinical Features

Sjogren syndrome encompasses a wide clinical spectrum

from specific

autoimmune exocrinopathy to a systemic disorder

characterized by

multiple

organ failure, including the kidney, nervous, and

musculoskeletal

systems.

The illness is caused by a CD4 T lymphocyte

infiltration of lacrimal

and

salivary glands. Namekawa et al further characterized

the areas of

salivary

gland destruction to contain CD4+CD28- cytotoxic T

lymphocytes.[5] The

disease starts insidiously, with increasing dryness of

the eyes and

mouth.

Individuals describe the feeling of having sand in

their eyes, whereas

others notice increasing difficulty with eating dry

foods, such as

bread or

crackers.

Extraglandular manifestations of Sjogren syndrome

include fatigue and

musculoskeletal pain. Strombeck et al[6] presented a

visual analog pain

scale and Short Form 36 data obtained from patients

with primary

Sjogren

syndrome, rheumatoid arthritis, and fibromyalgia. The

patients with

Sjogren

syndrome had a significant decrease in quality of life

similar to those

of

the rheumatoid arthritis and fibromyalgia groups,

which was related to

the

degree of pain felt by these individuals.

In regard to Sjogren syndrome and arthritis, Brennan

et al presented

data on

the frequency of sialadenitis and early synovitis in a

cohort of 10

patients.[7] Six individuals had positive lip biopsy

specimens, whereas

only

four had symptoms of xerostomia. The histologic biopsy

specimen

characteristics were similar for a control group of

patients with

Sjogren

syndrome and the subjects with early synovitis,

suggesting that the

arthritis associated with Sjogren syndrome may be

mediated by similar

cells

to those found in salivary glands.

Autoantibodies and Pathogenesis

The immune disorder associated with Sjogren syndrome

is characterized

by

B-cell activation, the production of multiple

autoantibodies, and the

loss

of immune tolerance. The antibodies correlate with

the extent and

severity

of disease in Sjogren syndrome and are potentially

involved in the

pathogenic development of autoimmune exocrinopathy.

Anti-Ro/SS-A and anti-La/SS-B are the clinically

important

autoantibodies in

primary Sjogren syndrome. Anti-Ro precipitins occur in

approximately

60% to

75% of primary Sjogren syndrome cases and are also

observed in cases of

secondary Sjogren syndrome.[8] The two Ro proteins

(Ro52 and Ro60)

localize

to surface membrane outcroppings on apoptotic cells,

and these blebs

may

become targets of the autoimmune response.[9] Anti-La

occurs in 40% of

patients with primary Sjogren syndrome. The La antigen

is a RNA

polymerase

I.[10]

Dr. Jonsson suggested that the pathogenic role of

anti-Ro and anti-La

in

Sjogren syndrome included the association among

leukopenia,

lymphopenia, and

hypogammaglobulinemia with more severe salivary

disease. An association

between surface expression of La on

conjunctival cells and aberrant expression pattern of

La on labial

salivary

glands exists in patients with Sjogren syndrome, as

does local salivary

production of anti-Ro and anti-La and the presence of

Ro52 and 60.

Additional proof of nonspecific B-cell activation may

be found in the

number

of autoantibodies produced by patients with Sjogren

syndrome. These

antibodies include those directed against carbonic

anhydrase,

proteasomal

subunits, and alpha-fodrin. Antiphospholipid

antibodies of the

immunoglobulin A isotype were reported in 20% of

patients with Sjogren

syndrome without signs of antiphospholipid syndrome,

but the clinical

importance of these antibodies remains to be

determined. In contrast,

the

presence of muscarinic M3 receptor antibodies that

decrease salivary

flow

may explain impaired glandular function in individuals

with less

extensive

lymphocytic infiltration of salivary glands.[11]

Immunopathogenesis and Apoptosis

The immunohistology of exocrine glands in Sjogren

syndrome shows a

predominant T-cell infiltration with fewer B cells and

macrophages. The

T

cells are thought to play a prominent role in the

destruction of

salivary

glands, but the exact mechanism of damage remains

unknown.

On recognition of a proper major histocompatibility

complex antigen

complex

on a target cell, cytotoxic T cells should induce cell

death by one of

two

independent pathways: the perforin-mediated or

Fas-mediated pathway.

However, apoptosis is deficient in the lymphocytes of

patients with

Sjogren

syndrome. Although the expression of fas, fasL,bcl-2,

and other

apoptosis-associated proteins has been detected in

minor salivary

glands

from patients with Sjogren syndrome,[12] studies have

shown a low

degree or

absence of cell death among infiltrating mononuclear

cells.[13] In

addition

to the damage caused by the absence of apoptosis,

injury to epithelial

cells

may also dampen the response of these cells to

muscarinic

stimulation.[14]

These damaged cells would explain the severe dryness

that was out of

proportion to the actual number of apoptotic cells

seen in salivary

gland

biopsy specimens. Glandular hypofunction is not solely

a result of the

destruction of salivary glands, because normal acinar

cells may be

observed

in patients with Sjogren syndrome, and lymphocytic

glandular

infiltration is

not always accompanied by decreased salivation.

Therapy

Treatment of Sjogren syndrome is directed at

decreasing the symptoms;

no

therapy is currently available to decrease lymphocytic

infiltration of

salivary glands or reverse the imbalance of apoptosis

of lymphocytes.

Oral

therapies are prescribed to increase the production of

saliva and

tears. A

study by LeVeque et al reported on the long-term

effect of pilocarpine

hydrochloride on increases in salivary flow in

patients with Sjogren

syndrome.[15] There were 212 patients with Sjogren

syndrome who

received 2.5

to 30 mg per day of pilocarpine during a 15-month

period. Increased

salivary

flow was sustained during the study without evidence

of tachyphylaxis.

Adverse events were limited to sweating in 49%,

urinary frequency in

16.5%,

flushing in 11.3%, and chills in 8%. Pilocarpine is

safe and effective

therapy for xerostomia associated with Sjogren

syndrome.

For dry eye symptoms, Tsubota et al[16] reported on

Cevimeline, a drug

studied in Japan. This drug is an analog of

acetylcholine chloride and

binds

preferentially to muscarinic M3 receptors. In a

double-blind study of

60

patients, 53% of the 19 patients taking 20 mg three

times daily and 53%

of

15 patients taking 30 mg three times daily

significantly improved

compared

with the placebo group. Eye symptoms decreased with

less eye pain, and

Rose

Bengal staining decreased at 2 weeks into therapy.

This preliminary

study

needs to be extended to document the continued

efficacy and safety of

this

agent for longer periods.

References

1. Sjogren H. Zur kenntnis der keratoconjunctivitis

sicca. Acta

Opthalmol.

1933;11(suppl 2):1-151.

2.Fox RI, C, Curd J, et al. Suggested

criteria for

classification.

Scand J

Rheumatol. 1986;61:28-30.

3.Manthorpe R, Oxholm P, Prause JU, et al. The

Copenhagen criteria for

Sjogren's

syndrome. Scand J Rheumatol. 1986;61:19-21.

4.Vitali C, Bombardieri S, Moutsopoulos H, et al.

Preliminary criteria

for

the

classification of Sjogren's syndrome: results of a

prospective

concerted

action

supported by the European community. Arthritis Rheum.

1993;36:340-347.

5.Strombeck B, Ekdahl C, sson L, Manthorpe R,

Wikstrom I.

Health-related

quality of life in primary Sjogren's syndrome,

rheumatoid arthritis and

fibromyalgia

compared to normal population data using SF-36.

Arthritis Rheum.

1999;42(suppl):S222.

6.Namekawa T, Matsumura R, Sumida T, et al.

Involvement of cytotoxic

CD4+

CD28-T cells in the tissue destruction of salivary

glands from patients

with

Sjogren's

syndrome. Arthritis Rheum. 1999;42(suppl):S140.

7.Reichlin M, Scofield RH. SS-A(Ro) autoantibodies.

In: JB,

Schoenfeld

Y, eds. Autoantibodies. Amsterdam, Netherlands:

Elsevier; 1996:789-797.

8.Brennan MT, Pilemer SR, Goldbach-Mansky R, et al.

Focal sialadenitis

in

patients

with early synovitis. Arthritis Rheum.

1999;42(suppl):S137.

9.Casciola-Rosen LA, Anhalt G, Rosen A. Autoantigens

targeted in

systemic

lupus

erythematosus are clustered in two populations of

surface structures on

apoptotic

keratinocytes. J Exp Med. 1994;179:1317-1330.

10.Chan EKL, Andrade LEC. Antinuclear antibodies in

Sjogren's syndrome.

Rheum Clin North Am. 1992;18:551-570.

11.Bacman S, LC, Sterin-Borda L, et al.

Autoantibodies against

lascrimal gland M3 muscarinic acetylcholine receptors

in patients with

primary Sjogren's syndrome. Invest Opthalmol Vis Sci.

1998;39:151-156.

12.Kong L, Ogawa N, Nakabayashi T, et al. Fas and Fas

ligand expression

in

the

salivary glands of patients with primary Sjogren's

syndrome. Arthritis

Rheum.

1997;40:87-97.

13.Nakamura H, Koji T, Tominaga M, et al. Apoptosis in

labial salivary

glands from

Sjogren's syndrome (SS) patients: companion with human

T lymphotropic

virus-I

(HTLV-I)-seronegative and -seropositive SS patients.

Clin Exp Immunol.

1998:114:106-112.

14.Masago R, Kong L, Aiba-Masago S, et al.

Fas-mediated signaling

abnormalities in salivary epithelial cells created by

aborted

apoptosis: a

model for SS. Arthritis

Rheum. 1999;42(suppl):S402.

15.LeVeque F, Khan Z, Salisbury PL, et al. Sustained

increases in

salivary

flow and safety findings following extended use of

pilocarpine tablets

for

the treatment of dry mouth symptoms in patients with

Sjogren's syndrome

(SS). Arthritis Rheum.

1999;42(suppl):S139.

16.Tsubota K, Ono M, Takamura E, et al. Efficacy of

civimeline, a

muscarinic

agonist in treating dry eye symptoms in patients with

Sjogren's

Syndrome.

Arthritis Rheum.

__________________________________________________

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American College of Rheumatology 1999 Annual

Scientific Meeting

[Medscape, 1999. © 1999 Medscape, Inc.]

Epidemiology, Diagnostics, and Management

Borenstein, MD

Sjogren syndrome was addressed in a State of the Art

Lecture by Roland

Jonsson, DMD,PhD, professor of immunology at the

University of Bergen

in

Norway. He reviewed the clinical manifestations and

research advances

associated with Sjogren syndrome and the presentation

of more than 40

abstracts.

Sjogren syndrome was named for the Swedish

ophthalmologist Henrik

Sjogren,

who first described the clinical and pathological

findings of

xerostomia

(dry mouth) and keratoconjunctivitis sicca (dry

eye).[1] Primary

Sjogren

syndrome is the disorder that occurs independent of

any additional

connective tissue disease, whereas secondary

Sjogren syndrome occurs in the setting of other

connective tissue

diseases,

such as rheumatoid arthritis, systemic lupus

erythematosus, or

polymyositis.

Epidemiology

Sjogren syndrome is a disease that affects all

populations throughout

the

world and occurs in all age groups. The peak incidence

is in the fourth

and

fifth decades of life, with a female-male ratio of

9:1. The prevalence

of

primary Sjogren syndrome varies from 0.08% in a

population study in

California to 2.7% in Sweden,[2,3] with an average

prevalence of 0.2%.

The

variation in frequency of the illness in these

population studies may

be

explained in part by different classification

criteria. The variation

in

other associated illnesses, such as lymphoma,

demyelinating disorders,

or

vasculitis, may also result from a lack of agreement

on diagnostic

criteria.

Classification Criteria

The most recent European criteria from 1993[4] include

an emphasis on

patients' subjective complaints. The criteria include

the presence of

four

of six symptoms, including (1) ocular symptoms, (2)

oral symptoms, (3)

evidence of keratoconjunctivitis sicca, (4) focal

sialadenitis by minor

salivary gland involvement, (5) instrumental evidence

of salivary gland

involvement, and (6) presence of autoantibodies.

Ocular symptoms include dry eyes for more than 3

months, recurrent

sensation

of sand or gravel in the eyes, or use of tear

substitutes more than

three

times a day. Oral symptoms include the daily feeling

of dry mouth for

more

than 3 months, recurrent or persistent swollen

salivary glands, or use

of

liquid to aid in swallowing dry food. Ocular signs are

characterized by

a

positive result on the Shirmer test (<5 mm in 5

minutes) or a Rose

Bengal

staining score of more than 4 according to the van

Bijsterveld scoring

system. Focal sialadenitis is distinguished by

lymphoid infiltration

in

exocrine glands.

The grading system of 1 to 4 corresponds to increasing

lymphocytic

infiltration with increasing destruction of salivary

gland structures.

Objective salivary gland testing includes salivary

scintigraphy,

parotid

sialography, or unstimulated salivary flow (<1.5 mL in

15 minutes).

Antibodies to Ro(SS-A) or La(SS-B), antinuclear

antibodies, and

rheumatoid

factors are associated with Sjogren syndrome. For

primary Sjogren

syndrome,

the presence of four of six criteria has a sensitivity

of 93.5% and

specificity of 94.0%.

The San Diego criteria for Sjogren syndrome include

manifestations of

both

primary and secondary Sjogren syndrome. Primary

Sjogren syndrome is

characterized by the following:

1. Symptoms and objective signs of ocular

dryness (Schirmer test

result of <8-mm wetting per 5 minutes and positive

Rose Bengal staining

of

cornea or conjunctiva to demonstrate

keratoconjunctivitis sicca).

2. Symptoms and objective signs of dry mouth

(decreased parotid

flow

rate using Lashley cups and abnormal findings on

biopsy specimen of

minor

salivary gland, with a focus score of >2 based on an

average of four

evaluable lobules).

3. Serologic evidence of systemic autoimmunity

(elevated

rheumatoid

factor >1:320 or elevated antinuclear antibody >1:320

or presence of

anti-SS-A[Ro] or anti-SS-B[La]antibodies).

Secondary Sjogren syndrome is defined by

characteristic signs and

symptoms

of Sjogren syndrome plus clinical features of

rheumatoid arthritis,

systemic

lupus erythematosus, polymyositis, scleroderma, or

biliary cirrhosis.

The

European and San Diego classification systems are the

two most

currently

referenced criteria.

Clinical Features

Sjogren syndrome encompasses a wide clinical spectrum

from specific

autoimmune exocrinopathy to a systemic disorder

characterized by

multiple

organ failure, including the kidney, nervous, and

musculoskeletal

systems.

The illness is caused by a CD4 T lymphocyte

infiltration of lacrimal

and

salivary glands. Namekawa et al further characterized

the areas of

salivary

gland destruction to contain CD4+CD28- cytotoxic T

lymphocytes.[5] The

disease starts insidiously, with increasing dryness of

the eyes and

mouth.

Individuals describe the feeling of having sand in

their eyes, whereas

others notice increasing difficulty with eating dry

foods, such as

bread or

crackers.

Extraglandular manifestations of Sjogren syndrome

include fatigue and

musculoskeletal pain. Strombeck et al[6] presented a

visual analog pain

scale and Short Form 36 data obtained from patients

with primary

Sjogren

syndrome, rheumatoid arthritis, and fibromyalgia. The

patients with

Sjogren

syndrome had a significant decrease in quality of life

similar to those

of

the rheumatoid arthritis and fibromyalgia groups,

which was related to

the

degree of pain felt by these individuals.

In regard to Sjogren syndrome and arthritis, Brennan

et al presented

data on

the frequency of sialadenitis and early synovitis in a

cohort of 10

patients.[7] Six individuals had positive lip biopsy

specimens, whereas

only

four had symptoms of xerostomia. The histologic biopsy

specimen

characteristics were similar for a control group of

patients with

Sjogren

syndrome and the subjects with early synovitis,

suggesting that the

arthritis associated with Sjogren syndrome may be

mediated by similar

cells

to those found in salivary glands.

Autoantibodies and Pathogenesis

The immune disorder associated with Sjogren syndrome

is characterized

by

B-cell activation, the production of multiple

autoantibodies, and the

loss

of immune tolerance. The antibodies correlate with

the extent and

severity

of disease in Sjogren syndrome and are potentially

involved in the

pathogenic development of autoimmune exocrinopathy.

Anti-Ro/SS-A and anti-La/SS-B are the clinically

important

autoantibodies in

primary Sjogren syndrome. Anti-Ro precipitins occur in

approximately

60% to

75% of primary Sjogren syndrome cases and are also

observed in cases of

secondary Sjogren syndrome.[8] The two Ro proteins

(Ro52 and Ro60)

localize

to surface membrane outcroppings on apoptotic cells,

and these blebs

may

become targets of the autoimmune response.[9] Anti-La

occurs in 40% of

patients with primary Sjogren syndrome. The La antigen

is a RNA

polymerase

I.[10]

Dr. Jonsson suggested that the pathogenic role of

anti-Ro and anti-La

in

Sjogren syndrome included the association among

leukopenia,

lymphopenia, and

hypogammaglobulinemia with more severe salivary

disease. An association

between surface expression of La on

conjunctival cells and aberrant expression pattern of

La on labial

salivary

glands exists in patients with Sjogren syndrome, as

does local salivary

production of anti-Ro and anti-La and the presence of

Ro52 and 60.

Additional proof of nonspecific B-cell activation may

be found in the

number

of autoantibodies produced by patients with Sjogren

syndrome. These

antibodies include those directed against carbonic

anhydrase,

proteasomal

subunits, and alpha-fodrin. Antiphospholipid

antibodies of the

immunoglobulin A isotype were reported in 20% of

patients with Sjogren

syndrome without signs of antiphospholipid syndrome,

but the clinical

importance of these antibodies remains to be

determined. In contrast,

the

presence of muscarinic M3 receptor antibodies that

decrease salivary

flow

may explain impaired glandular function in individuals

with less

extensive

lymphocytic infiltration of salivary glands.[11]

Immunopathogenesis and Apoptosis

The immunohistology of exocrine glands in Sjogren

syndrome shows a

predominant T-cell infiltration with fewer B cells and

macrophages. The

T

cells are thought to play a prominent role in the

destruction of

salivary

glands, but the exact mechanism of damage remains

unknown.

On recognition of a proper major histocompatibility

complex antigen

complex

on a target cell, cytotoxic T cells should induce cell

death by one of

two

independent pathways: the perforin-mediated or

Fas-mediated pathway.

However, apoptosis is deficient in the lymphocytes of

patients with

Sjogren

syndrome. Although the expression of fas, fasL,bcl-2,

and other

apoptosis-associated proteins has been detected in

minor salivary

glands

from patients with Sjogren syndrome,[12] studies have

shown a low

degree or

absence of cell death among infiltrating mononuclear

cells.[13] In

addition

to the damage caused by the absence of apoptosis,

injury to epithelial

cells

may also dampen the response of these cells to

muscarinic

stimulation.[14]

These damaged cells would explain the severe dryness

that was out of

proportion to the actual number of apoptotic cells

seen in salivary

gland

biopsy specimens. Glandular hypofunction is not solely

a result of the

destruction of salivary glands, because normal acinar

cells may be

observed

in patients with Sjogren syndrome, and lymphocytic

glandular

infiltration is

not always accompanied by decreased salivation.

Therapy

Treatment of Sjogren syndrome is directed at

decreasing the symptoms;

no

therapy is currently available to decrease lymphocytic

infiltration of

salivary glands or reverse the imbalance of apoptosis

of lymphocytes.

Oral

therapies are prescribed to increase the production of

saliva and

tears. A

study by LeVeque et al reported on the long-term

effect of pilocarpine

hydrochloride on increases in salivary flow in

patients with Sjogren

syndrome.[15] There were 212 patients with Sjogren

syndrome who

received 2.5

to 30 mg per day of pilocarpine during a 15-month

period. Increased

salivary

flow was sustained during the study without evidence

of tachyphylaxis.

Adverse events were limited to sweating in 49%,

urinary frequency in

16.5%,

flushing in 11.3%, and chills in 8%. Pilocarpine is

safe and effective

therapy for xerostomia associated with Sjogren

syndrome.

For dry eye symptoms, Tsubota et al[16] reported on

Cevimeline, a drug

studied in Japan. This drug is an analog of

acetylcholine chloride and

binds

preferentially to muscarinic M3 receptors. In a

double-blind study of

60

patients, 53% of the 19 patients taking 20 mg three

times daily and 53%

of

15 patients taking 30 mg three times daily

significantly improved

compared

with the placebo group. Eye symptoms decreased with

less eye pain, and

Rose

Bengal staining decreased at 2 weeks into therapy.

This preliminary

study

needs to be extended to document the continued

efficacy and safety of

this

agent for longer periods.

References

1. Sjogren H. Zur kenntnis der keratoconjunctivitis

sicca. Acta

Opthalmol.

1933;11(suppl 2):1-151.

2.Fox RI, C, Curd J, et al. Suggested

criteria for

classification.

Scand J

Rheumatol. 1986;61:28-30.

3.Manthorpe R, Oxholm P, Prause JU, et al. The

Copenhagen criteria for

Sjogren's

syndrome. Scand J Rheumatol. 1986;61:19-21.

4.Vitali C, Bombardieri S, Moutsopoulos H, et al.

Preliminary criteria

for

the

classification of Sjogren's syndrome: results of a

prospective

concerted

action

supported by the European community. Arthritis Rheum.

1993;36:340-347.

5.Strombeck B, Ekdahl C, sson L, Manthorpe R,

Wikstrom I.

Health-related

quality of life in primary Sjogren's syndrome,

rheumatoid arthritis and

fibromyalgia

compared to normal population data using SF-36.

Arthritis Rheum.

1999;42(suppl):S222.

6.Namekawa T, Matsumura R, Sumida T, et al.

Involvement of cytotoxic

CD4+

CD28-T cells in the tissue destruction of salivary

glands from patients

with

Sjogren's

syndrome. Arthritis Rheum. 1999;42(suppl):S140.

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  • 2 years later...
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It is Sjoegren's syndrome - a comprehensive and unpleasant auto-immune

condition.

Let's see what the various suggestions are for this!

Savage MA RSHom FSHom

26 Winstanley Road

Saffron Walden

Essex CB11 3EQ

01799 524442 Mobile: 07889 989398

Email: roger.jo@...

Sjpgren syndrome

Hi-Have anyone ever heard of the above syndrome. I have never been

diagnosed with it but I have all the symtoms and an auto immune

disease too. If you have had any experience in treating it with QXCI

I would like to hear from you. Thanks.

.............................................

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  • 8 years later...
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Thanks Ebtessam and RasheedaYes from that point of view you are right But I read in scully that in sjogren ,lymphocytes and plasma cell infiltrate salivary glands making acinar destruction.Doesn't that make it type 4 then? What do you think? Other opinions please?BalsamSent from my iPadOn 1 Apr 2012, at 12:59, ebtessam elhamalawy <ebtessamhamalawy@...> wrote:

hi basmala I believe its type 3 CHCH BY IMMUNOCOMPLEX FORMAITON THAT AFFECTS MULTIPLE ORGANSBEST REGARDSEBTISAM From: Balsam_Majid <balsam_majid@...> " " < > Sent: Sunday, 1 April 2012, 12:08 Subject: Sjogren syndrome

What type of hypersensitivity is sjogren syndrome plz?

Sent from my iPad

=

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